QUAD #22: What is CHARGE syndrome? with Dr. Catherine Hart

Stay Current in Pediatric Surgery by StayCurrent: Pediatric Surgery

Episode notes

In this educational video, Dr. Catherine Hart, ENT surgeon at Cincinnati Children’s, provides an overview of CHARGE syndrome, a rare genetic disorder that affects multiple organ systems. Learn about its diagnosis, clinical features, and the comprehensive care required for patients with this condition.

Key Highlights:

  • What is CHARGE Syndrome? The acronym stands for coloboma, heart defects, atresia of the choanae, retardation of growth and development, genital/urinary anomalies, and ear malformations.
  • Causes and Diagnosis: CHARGE is typically caused by a CHD7 mutation on chromosome 8 but can also be diagnosed clinically with specific major and minor criteria.
  • Multisystem Impact: The syndrome’s highly variable expression means it can affect almost ev ... 
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Keywords
pediatric surgerysome4pedsurgquadaerodigestiveentCHARGEcolombasyndromeheart defectsatresia of the choanaeretardation of growth and developmentgenital anomaliesurinary anomaliesear malformationsrare genetic disorderCHD7 mutationchromosome 8airway feedingdevelopmental challenges